Abstract

MALDONADO GARCIA, Edwin Leopoldo et al. Multiple Endocrine Neoplasia IIA: Bilateral Pheochromocytoma. About a Case and Literature Review. Rev. Fac. Med. (Méx.) [online]. 2021, vol.64, n.1, pp.26-31.  Epub July 06, 2021. ISSN 2448-4865.  https://doi.org/10.22201/fm.24484865e.2021.64.1.04.

We present the case of a 54-year-old female patient with a family history of multiple endocrine neoplasia type II, with a genetic study for MEN 2 IIA EXON 11, CG6B c634, onset with hypertensive heart disease and diastolic dysfunction, tomographic finding of bilateral adrenal tumor by imaging. A conventional transabdominal adrenalectomy was performed, finding a right tumor with a capsule corresponding to pheochromocytoma with a weight of 1,100 g of 14.5 cm of greater diameter with invasion of the capsule without breaking it, and a left adrenal tumor corresponding to pheochromocytoma with a weight of 950 g of 15 cm of greater diameter.

Keywords : Pheochromocytoma; Multiple endocrine neoplasia; adrenalectomy; retroperitoneum; adrenal gland.