Abstract

RIVEROS-RAMOS, Lizbeth Carolina et al. Primitive neuroectodermal tumor of the pancreas. Case report and review of the literature. Acta pediatr. Méx [online]. 2016, vol.37, n.1, pp.26-31. ISSN 2395-8235.

The primitive neuroectodermal tumor of the pancreas, are small round cell tumors arising from the soft tissue that belongs to the family of Ew-ing's sarcoma, The primary neuroectodermal (PNET) of the pancreas is very rare, have been reported only 17 cases in the literature. We report the case of a 9 year-old female patient, with PNET of the pancreas, was carried out a Whipple surgery, and began chemotherapy treatment with, vincristine, doxorubicin Pegylated, etoposide and ifosfamide and radiation therapy. Currently, the patient is in monitoring since March 2013, with a follow up of 23 months, overall in good condition and without evidence of tumor activity.

Keywords : Primitive Neuroectodermal tumor; Primitive neuroectodermal tumor of the pancreas; Whipple procedure.