Abstract

QUISBERT-CRUZ, R  and  ZARATE-MONDRAGON, F. Infant hypertensive emergency secondary to autosomic recessive polycystic kidney disease. Case report. Acta pediatr. Méx [online]. 2017, vol.38, n.4, pp.237-243. ISSN 2395-8235.  https://doi.org/10.18233/apm38no4pp237-2431432.

Polycystic kidney disease associated with congenital hepatic fibrosis is an inherited disease; it is within the spectrum of diseases hepatorenal fibrocystic. Its estimated frequency is 1 in 20,000 live births for the variety of autosomal recessive polycystic kidney disease and rarer for autosomal dominant variety. One case report is presented about a patient whose illness began with a difficult control hypertensive crisis arises due to polycystic kidney disease and congenital hepatic fibrosis, a rare clinical presentation. Include the importance of controlling blood pressure to prevent complications due to high blood pressure as cardiac hypertrophy, heart failure and chronic retinopathy.

Keywords : polycystic kidney disease; congenital liver disease; hypertensive emergency; ductal plate.