BACKGROUND:

Desmoid tumors are rare, monoclonal, soft tissue neoplasms arising from mesenchymal stem cells. They are locally aggressive tumors, reaching large sizes and with a high recurrence rate if excision is not complete.

CLINICAL CASE:

63-year-old female patient consulted due to the appearance of a vulvar tumor of about 20 cm in diameter that had grown slowly and progressively. The tumor reached the left labia majora and labia minora, the mons pubis, the perineal and left inguinal regions. Ultrasound, nuclear magnetic resonance and biopsy studies were performed. The initial biopsy concluded that it was a desmoid tumor, so it was decided to perform excision with wide safety margins. V-Y advancement flaps were used to close the large defect. The pathological anatomy of the specimen confirmed that it was a benign mesenchymal tumor, compatible with leiomyoma. The evolution of the patient has been very satisfactory.

CONCLUSIONS:

As in many diseases, the anatomopathological diagnosis is decisive, especially in the case of tumors that share morphological characteristics in order not to hinder the diagnostic and therapeutic orientation. Complete excision with wide margins as definitive treatment and to avoid recurrences is fundamental.