Objective:

To present the case of a patient with choledochal cyst and its treatment, due to its low frequency and the high risk of developing cholangiocarcinoma. Presentation: A 26-year-old female with clinical signs of abdominal pain in the right hypochondrium and epigastrium, intolerance to cholecystokinetics, conjunctival jaundice, arrived to urgency with treatment analgesics, USG reporting normal vesicle, normal liver, proximal choledocholum 7 mm, dilated distal common bile duct of 35 mm with microliths inside, are admitted to the floor requesting exams reporting CBC, BC, TP, normal TPT, normal LFT, ERCP is reported, and type I choledochal cyst is scheduled for surgical intervention With the resection of the choledochal cyst and cholecystectomy as well as Roux-en-Y hepaticojejunostomy with prolene 3-0, a 6 x 4 cm choledochal cyst is found ranging from the common hepatic to pancreas, evolving satisfactorily, tolerating the oral route on the fourth day of surgery, leaving on the 7th day, is seen in the consultation, with discomfort of the surgery; being anicteric and with well-healed surgical wound, normal control USG. Control exams with normal CBC, BC, TP, TPT and LFT.

Conclusions:

It is an infrequent condition. One is found in 100,000 to 150,000, predominantly in Asian countries 20 to 30% is diagnosed in adults. It has a high incidence of developing cholangiocarcinoma, hence the importance of cyst resection. Type I continues to be the most frequent, reporting in the world literature.