Abstract

SANCHEZ DE LEON-CORRAL, M et al. Ribbing disease: apropos of a case. Acta ortop. mex [online]. 2023, vol.37, n.2, pp.113-117.  Epub May 06, 2024. ISSN 2306-4102.  https://doi.org/10.35366/112992.

Ribbing’s disease is a rare form of sclerosing bone dysplasia characterized by exuberant yet benign endosteal bone, and periosteum formation in the diaphysis of long bones. Diagnosis relies on exclusionary criteria, as the primary clinical manifestations entail progressive pain unresponsive to analgesic therapy, accompanied by serological markers within normal ranges. Pain management constitutes the cornerstone of treatment, with surgery appearing to offer the most efficacious approach, despite the absence of a standardized therapeutic algorithm. The diagnostic and therapeutic delays associated with Ribbing’s disease, reaching up to 16 years, exert a profound impact on patients’ quality of life. Hence, the purpose of our work is to present a case report of Ribbing’s disease and conduct a comprehensive literature review on the subject matter.

Keywords : Ribbing disease; bone dysplasia; diagnosis; pain; treatment.

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