Abstract

PETROVIC, Igor et al. Rupture of suppurated liver hematoma into the anterior abdominal wall in a patient with Rendu-Osler-Weber syndrome. Cir. cir. [online]. 2020, vol.88, suppl.2, pp.66-70.  Epub Feb 08, 2022. ISSN 2444-054X.  https://doi.org/10.24875/ciru.20000342.

We report a case of ruptured liver hematoma as a result of suppurated arteriovenous malformation (AVM) in a patient with Rendu-Osler-Weber (ROW) syndrome. The patient presented with unexplained fever and upper right abdominal pain associated with microcytic anemia. A computed tomography scan revealed increasing subcapsular liver hematoma and features of liver abscess. Intraoperatively, a left liver hematoma mixed with pus was found that was attached to the anterior abdominal wall. Surgery included left lateral bisegmentectomy, while pathohistological analysis showed AVM and genetic tests confirmed ROW. This is the first such life-threatening surgical case of ROW complication reported in the scientific literature.

Keywords : Rendu-Osler-Weber syndrome; Liver abscess; Liver rupture; Hereditary telangiectasia.

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