Abstract

VILLARINO-GALVAN, J; GUTIERREZ-ORTEGA, A; PENA-OLVERA, S  and  MANCERA-ELIAS, G. Orotracheal intubation using Airtraq in a pediatric patient with Treacher Collins syndrome. Anest. Méx. [online]. 2019, vol.31, n.2, pp.91-96. ISSN 2448-8771.

The Treacher Collins syndrome (SCT) also known as Franceshetti syndrome or mandibulofacial dysostosis is a congenital malformation in the craniofacial development. Autosomal dominant disease, is the result of the mutation of the TCOF1 gene. Its incidence is estimated in 1 in every 50,000 live births. Characterized by presenting maxillary, zygomatic, mandibular hypoplasia; combined with an oral diminished opening, abnormalities in the temporomandibular joint and in some cases cleft palate. Due to all these characteristics, patients with a difficult airway where adequate ventilation and endotracheal intubation might become a critical scenario for the anesthesiologist increasing the perioperative morbidity and mortality of this age group. SCT is associated to difficult intubation, so having a strategy adapted to the availability and experience of the devices found in our environment will make the results become optimal. We present the case of a five year old female patient with the diagnosis of Treacher Collins syndrome programmed to have performed esophageal dilatations with an airway approach using the pediatric Airtraq device.

Keywords : Treacher Collins Syndrome; videolaringoscopio Airtrq; difficult airway.