Abstract

ROBLES-DIAZ, José F.. Desmoid-type fibromatosis retroperitoneal aggressive and gigant in Peru: Case report and literature review. Gac. mex. oncol. [online]. 2022, vol.21, suppl.1, pp.72-78.  Epub Sep 11, 2023. ISSN 2565-005X.  https://doi.org/10.24875/j.gamo.22000088.

Desmoid-type fibromatosis retroperitoneal is a rare, slow-growing, recurrent neoplasm without metastasis. The treatment of fibromatosis is currently proposed by active surveillance, however, due to the retroperitoneal location, there is a risk of mortality and losing the therapeutic option of active management. Being the established treatment, the complete or incomplete surgical resection. The subject is reviewed regarding the case in a 48-year-old man, a native of the central Peruvian jungle, without a traumatic history, with giant retroperitoneal fibromatosis. Being proposed to undergo incomplete resection followed by adjuvant with irradiation.

Keywords : Retroperitoneum; Aggressive fibromatosis; Desmoid tumor; Desmoid-type fibromatosis; β-catenin; Radiotherapy.