Introduction:

This is a non-hereditary, very rare syndrome, present since birth or youth; it is due to an alteration in the chromosome 20. The objective of this work is to present the case of a male adolescent who consulted because of an ulcer in the sole of the right foot; he also showed signs of this syndrome.

Case report:

16-year-old male who lived in a distant rural zone; he complained of an ulcer in the sole of the right foot for several months. There was shortness of the right lower extremity, cafe-au-lait pigmented skin lesions, abnormal development of limbs and alopecia areata of the scalp. Cleaning of the ulcer, bandages, sole protector, and rest were recommended. A future work-up with X rays and consultations was planned, but he never came back. Later, he changed his address. Clinical findings were the basis of the diagnosis of McCune-Albright syndrome.