Resumen

GAMBOA-SALCEDO, Tamara; CARDOSO-HERNANDEZ, Gabriel; SAUCEDO-RAMIREZ, Omar Josué  y  PENA-ALONSO, Yolanda Rocío. Burkholderia cepacia and chronic granulomatous disease: a case report. Bol. Med. Hosp. Infant. Mex. [online]. 2009, vol.66, n.1, pp.68-75. ISSN 1665-1146.

Introduction. Chronic granulomatous disease (CGD) is an immunodeficiency characterized by a defect of phagocitosis, so initial manifestations are those from the secondary infection. It is an uncommon disease, whose diagnosis is always a challenge. Case report. The case of a previously healthy boy who came to the hospital with fever of unknowns origin is presented. He was diagnosed with persistent pneumonia that required decortication. Burkholderia cepacia grew from the lung biopsy culture. Because this bacteria has been related to immunodeficient patients, screening for immunodeficiency were performed and the diagnosis of CGD was established. Conclusion. Immunodeficiency should be ruled out in patients with infections due to B. cepacia.

Palabras llave : Burkholderia cepacia; granulomatous disease; chronic; inmunocompromised host; child.