Introduction:

Porto-pulmonary hypertension refers to pulmonary arterial hypertension (mean pulmonary artery pressure > 25 mmHg at rest and pulmonary capillary wedge pressure < 15 mmHg) associated with portal hypertension; it is a recognized complication of chronic liver disease.

Case report:

85-year-old female with a 3-year course characterized by edema of pelvic limbs, and one month with dry cough, progressive dyspnea and anasarca, on examination: pulmonary basal esters, second pulmonary noise reinforcement. Abdomen with collateral venous network, ascites and anasarca, with oximetry of 84%, electrocardiogram and echocardiography confirmed pulmonary arterial hypertension and abdominal tomography, ascites and dilatation of suprahepatic veins. Managed with diuretics, albumin and phosphodiesterase inhibitors, its evolution was towards clinical and functional improvement.

Conclusion:

Porto-pulmonary hypertension is an entity with systemic repercussion and poor prognosis, its treatment is still under investigation.