Resumen

GUEVARA-CANCECO, Ana Patricia Georgina et al. Double-orifice mitral valve in an asymptomatic young adult woman with aortic coarctation and bicuspid aortic valve. Cardiovasc. metab. sci [online]. 2022, vol.33, n.1, pp.17-20.  Epub 22-Mayo-2023. ISSN 2954-3835.  https://doi.org/10.35366/104033.

Congenital heart disease in Mexico ranks second among congenital malformations in newborns, with an incidence of 0.8-1.4%. Double orifice mitral valve (DOMV) is rare congenital heart disease, with a reported incidence of 0.05%. This malformation consists of the anatomical presentation of two mitral orifices, commonly associated with other congenital malformations such as septal defects, complete or partial malformations of the atrioventricular canal, aortic coarctation, tetralogy of Fallot, atrial or interventricular communication, Ebstein’s anomaly and patent ductus arteriosus. The clinical characteristics are variable and can even go unnoticed and be diagnostic until adulthood. We present the case of an asymptomatic young woman with a diagnosis of arterial hypertension. During a routine control was diagnosed with multiple congenital heart diseases whose relationship is little described in the literature, this being the third case reported. At present, multimodal imaging techniques allow a greater characterization of lesions of both the valve and the valve apparatus, intending to carry out a comprehensive diagnostic and therapeutic approach to offer the greatest benefit to the patient.

Palabras llave : Double-orifice mitral valve (DOMV); congenital malformations; multimodal imaging techniques.