Introduction:

Prenatal ultrasonographic now represents a form of presentation of congenital bronchopulmonary malformations (CBPM), these intrathoracic lesions can cause polyhydramnios, mediastinal shift, hydrops and fetal death, it presents the first national report and process engineering EXIT described (ex utero intrapartum) as an option for these fetal lung masses high risk. Description of cases: Fetus 30 SG with a microcystic mass of the entire left lung with mediastinal shift and fetal hydrops, with a CVR 2.7, the pregnancy was carried to term and procedure EXIT is carried out with the support of utero flow successful placental 63 minutes with selective intubation of right bronchus by rigid bronchoscopy and left pneumonectomy a solid lesion compatible with MAQ type I diffuse and isolated pockets of type 0, patient died from pulmonary complications associated with barotrauma and hypoplasia and hypertension refractory to management conventional.

Discussion:

The EXIT procedure in our area may represent a therapeutic option for high-risk MCBP persistent near-term birth mediastinal deviation; the diffuse involvement of the affected lung, contralateral pulmonary hypoplasia and pulmonary hypertension refractory remain the defining factors perinatal mortality.