Resumo

GODINEZ BARRAGAN, Mariana; PARES VIDRIO, Gustavo; HINOJOSA AGUIRRE, Alejandro  e  YAMAMOTO NAGANO, Adolfo. Adams-Oliver syndrome: Case report. Rev. Odont. Mex [online]. 2011, vol.15, n.3, pp.175-182. ISSN 1870-199X.

Adams Oliver syndrome (AOS) is a rare disease characterized by congenital scalp defects, terminal transverse limb malformations, and cutis marmorata telangiectatica, whose treatment requires a multidisciplinary focus to improve the patient s quality of life. We report the case of a child afflicted with varied manifestations of AOS including craniofacial alterations in the form of facial fissure, bilateral cleft lip and grade III cleft palate. Therapeutic focus of this case was approached in the dental area, taking into account the patient s systemic conditions. The process was divided into five phases taking into consideration the patient s current age, as well as intraoral and craniofacial circumstances.

Palavras-chave : Adams Oliver syndrome; aplasia cutis congenita terminal transverse limb defects.

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