Resumo

CORTES-VAZQUEZ, Yeniseik D. et al. Renal carcinoma papilar type 2, associated with piloleiomiomatosis and bilateral Leydig cell testicular tumors. Cir. cir. [online]. 2020, vol.88, suppl.2, pp.94-98.  Epub 08-Fev-2022. ISSN 2444-054X.  https://doi.org/10.24875/ciru.20001487.

10-15% of cases of renal tumors correspond to papillary type, the association to hereditary syndromes is rare, and aggressive. Clinical case: male with a history of piloleiomyomatosis and right kidney and left adrenal tumor, right radical nephrectomy with papillary renal carcinoma type 2. Development retroperitoneal, hepatic and bilateral testicular tumor. Left radical orchiectomy with Leydig cell tumor, hepatic and retroperitoneal metastasectomy with papillary carcinoma metastasis type 2, latest follow-up study without tumor activity.

Palavras-chave : Papillary renal cancer; Leiomyomatosis; Pyeloleiomyomatosis; Leydig cell tumor.